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KMID : 0032220200320050426
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Annals of Dermatology
2020 Volume.32 No. 5 p.426 ~ p.429
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A Case of Pseudomyogenic Hemangioendothelioma of the Lower Extremity
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Choi Myoung-Eun
Lim Dong-Jun
Chang Sung-Eun
Lee Mi-Woo
Choi Jee-Ho
Lee Woo-Jin
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Abstract
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Pseudomyogenic hemangioendothelioma (PMH) is a rare vascular tumor and was recently recognized as a distinct entity. It has a predilection for young male adults and it frequently occurs in distal extremities. Although it is known to follow an indolent course, multi-focal presentation and local recurrence are common. PMH should be differentiated from epithelioid sarcoma, epithelioid hemangioendothelioma, dermatofibrosarcoma protuberans, and rhabdomyosarcoma. Its characteristic immunohistochemical staining pattern and recurrent translocation t(7:19)(q22:q13) are the basis for its diagnosis. Surgical excision is the mainstay treatment, although chemotherapy can be considered in non-operable patients. We present a rare case of a 40-year-old Korean male patient diagnosed with PMH through an excisional biopsy to facilitate the recognition PMH in the clinical practice.
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KEYWORD
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Epithelioid cells, Hemangioendothelioima, Leg, Soft tissue neoplasms
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